Desmoid Fibromatosis: A Neonatal Presentation

International Journal of Research in Health Sciences,2016,4,3,77-80.
Published:July 2016
Type:Case Report
Authors:
Author(s) affiliations:

Varun Hathiramani1, ShrutiTewari2, AnantBangar3, VikramMardhekar4, Rajeev G Redkar5

16th year resident, 21st year Resident, 3Junior Consultant, 4Consultant Pediatrician and Neonatologist, 5Consultant Pediatric Surgeon, Department of Pediatric Surgery,Lilavati Hospital and Research Centre, Mumbai, INDIA.

Abstract:

Desmoid tumors describe a rare monoclonal, fibroblasticproliferation characterized by a variable and oftenunpredictable clinical course. Although histologicallybenign, desmoids are locally invasive and associatedwith a high local recurrence rate, but lack metastaticpotential.Although desmoid tumors are more common in persons aged 10-40 years than in others, they do occur in young children and older adults, but have rarely been reported in the neonatal age group. We report here a 17 day child who presented with a cervical swelling whose histology was desmoid fibromatosis.

Clinical picture showing swelling in left supra-calvicular region