Double lip is a rare developmental anomaly which usually involves the upper lip than lower lip. Infrequently it may be seen in upper and lower lips concurrently. It may be congenital or acquired. Its occurrence in isolation or as a constituent of Ascher’s syndrome is well documented. Congenital double lip is a rare oral anomaly. Surgical treatment is indicated more often for aesthetic reasons when the excess tissue interferes with functionality. The results are generally very good and complications are extremely rare. We describe a case of young boy presenting with congenital upper double lip, along with etiology, clinical presentation and treatment plan and review of literature. Congenital maxillary double lip is one of the unusual forms of lip abnormality. It not only interferes with speech and mastication but also affects the facial aesthetic. Though aesthetic is prime concern, surgical correction of the anomaly may be required to assist speech and mastication.